Epithelioid sarcoma: two variants of the same entity

Authors

  • Luca Garin Troyer General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Valeria Cecilia Orsi J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Ana Campastri J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Iris Barrio J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • César Chiappe J.M. Ramos Mejía Acute Hospital General, Autonomous City of Buenos Aires, Argentina
  • Guadalupe Ailín García General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Paula Bourren Dr. Juan A. Fernández General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Cecilia Eleonora Ventrice General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Ana Clara Acosta J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Keywords:

sarcomas, epithelioid sarcoma, INI1, SMARCB1

Abstract

Sarcomas are malignant neoplasms that originate from mesenchymal tissue. Epithelioid sarcoma is a rare variant of soft tissue sarcoma, representing approximately 1% of them. There are two variants: a distal type and a proximal one, with a high recurrence and metastasis rate.

Two cases of male patients with epithelioid sarcoma are presented, one with the distal variant and the other with the proximal variant.

Author Biographies

Luca Garin Troyer, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

Dermatologist, Department of Dermatology and Pathology

Valeria Cecilia Orsi, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Second Year Resident Physician, Dermatology and Pathology Service

Ana Campastri, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Dermatologist, Department of Dermatology and Pathology

Iris Barrio, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Dermatologist. Staff Physician, Dermatology and Pathology Department

César Chiappe, J.M. Ramos Mejía Acute Hospital General, Autonomous City of Buenos Aires, Argentina

Pathologist. Staff Physician, Dermatology and Pathology Service

Guadalupe Ailín García, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

Medical Pathologist, Department of Dermatology and Pathology

Paula Bourren, Dr. Juan A. Fernández General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Dermatologist. Head of Service, Dermatology and Pathology Service

Cecilia Eleonora Ventrice, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

Dermatologist and Pathologist. Staff Physician, Department of Dermatology and Pathology

Ana Clara Acosta, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Dermatologist. Staff Physician, Dermatology and Pathology Department

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Published

2022-09-01

Issue

Vol. 28 No. 3 (2022): July-September 2022

Section

Original Articles

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