Fibrosis angiocéntrica eosinofílica, enfermedad relacionada con IgG de cabeza y cuello

Hugo N. Cabrera; Silvia Pérez; María Fernanda Carriquiri; José Casasꝉ

Authors

Hugo N. Cabrera Faculty of Medicine of the University of Buenos Aires, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
Silvia Pérez Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
María Fernanda Carriquiri Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
José Casasꝉ Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Keywords:

angiocentric fibrosis, IgG related disease

Abstract

Eosinophilic angiocentric fibrosis is a fibrosing inflammatory condition of the upper airways, sinuses, orbit, salivary and lacrimal glands, with cutaneous involvement usually over the nose; there is nasal deformation and obstruction, with erythematous plaques on its surface. It is of rare observation; less than 60 cases have been published, and it is included within the group of IgG4-related diseases. We present the case of an adult woman with facial skin involvement and respiratory obstructive symptoms, with normal serum IgG4, and a satisfactory response to methotrexate.

Author Biographies

Hugo N. Cabrera, Faculty of Medicine of the University of Buenos Aires, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Emeritus Professor of Dermatology

Silvia Pérez, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Dermatologist

María Fernanda Carriquiri, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Dermatologist

José Casasꝉ, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Dermatopathologist

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