Venous ulcers due to infrarenal inferior vena cava agenesis and protein S deficiency

Authors

  • Ana Campastri Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina
  • Cindy Paula Frare Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina
  • Verónica Vallejo Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina
  • Mónica Jorge Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina
  • Rubén Eduardo Spiner Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

DOI:

https://doi.org/10.47196/da.v28i1.2184

Keywords:

inferior vena cava, agenesis, venous ulcers, protein S deficiency, thrombophilia

Abstract

Infrarenal inferior vena cava agenesis is a rare malformation. Although it is typically spotted through image findings, it may also manifest itself in dyspnea, cardiac failure, thrombosis, or ulcers. Connecting inferior vena cava agenesis with thrombophilia is extremely infrequent. There may be some causal relationship between both entities, which goes beyond mere coexistence. We present a patient with ulcers due to infrarenal inferior vena cava agenesis and protein S deficiency, showing favorable recovery with advanced wound healing and elastic compression treatment.

Author Biographies

Ana Campastri, Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

Dermatologist. Chief Resident

Cindy Paula Frare, Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

Dermatologist Doctor

Verónica Vallejo, Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

Hematologist Doctor

Mónica Jorge, Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

Staff Dermatologist. In charge of the Wound Sector

Rubén Eduardo Spiner, Acute General Hospital "José M. Ramos Mejía", Autonomous City of Buenos Aires, Argentina

Staff Dermatologist

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Published

2022-03-01

Issue

Section

Clinical Cases