Reticular erythematous mucinosis with good response to topical treatment

Authors

  • María Belén Elias Kairuz National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina
  • Hassibe Desiree Salich National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina
  • Jimena Agostina Miranda National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina
  • Marco Mario Mazzotta National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina
  • Ivana Laura Forni National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina
  • Lorena Andrea Cippitelli National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

DOI:

https://doi.org/10.47196/da.v26i4.2153

Keywords:

reticular erythematous mucinosis, cutaneous mucinosis, lupus erythematosus tumidus

Abstract

Reticular erythematous mucinosis is a rare form of cutaneous mucinosis of unknown etiology and incidence that predominates in middle-aged women. Clinic and histopathology are essential to arrive at the diagnosis. The first-line treatment is oral hydroxychloroquine, although good results have been described in the literature with topical treatments.

We present two patients diagnosed with reticular erythematous mucinosis, with good response to topical tacrolimus and corticosteroids, highlighting the safety and easy handling that it represents in this rare entity.

Author Biographies

María Belén Elias Kairuz, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Second Year Resident Physician, Postgraduate Dermatology Clinic. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

Hassibe Desiree Salich, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Second Year Concurrent Physician, Postgraduate Dermatology Clinic. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

Jimena Agostina Miranda, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Third Year Resident Physician, Postgraduate Dermatology Clinic. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

Marco Mario Mazzotta, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Pathologist. Adjunct Professor, Chair of Pathological Anatomy. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

Ivana Laura Forni, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Medical Adjunct Professor, Chair of the Dermatological Clinic. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

Lorena Andrea Cippitelli, National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba, Province of Córdoba, Argentina

Dermatologist Physician. Adjunct Professor, Chair of the Dermatological Clinic. National Hospital of Clinics, Faculty of Medical Sciences, National University of Córdoba.

References

I. Haendchen LC, Sabbag DS, Furlani Wde J, de Souza PK, et ál. Reticular erythematous mucinosis. Cutis 2014;93:22-24.

II. Steigleder GK, Gartmann H, Linker U. REM syndrome: reticular erythematous mucinosis (round-cell erythematosis), a new entity? Br J Dermatol 1974;91:191-199.

III. Del Pozo J, Peña C, Almagro M, Yebra MT, et ál. Systemic lupus erythematosus presenting with a reticular erythematous mucinosis-like condition. Lupus 2000;9:144-146.

IV. Thareja S, Paghdal K, Lien MH, Fenske NA. Reticular erythematous mucinosis - a review. Int J Dermatol 2012;51:903-909.

V. Suárez-Amor O, Pérez-Bustillo A, González-Morán MA, Ramírez-Santos A, et ál. Mucinosis eritematosa reticular: respuesta parcial al tratamiento con tacrolimus. Actas Dermosifiliogr 2010;101:105-106.

VI. Mansouri P, Farshi S, Nahavandi A, Safaie-Naraghi Z. Pimecrolimus 1 percent cream and pulsed dye laser in treatment of a patient with reticular erythematous mucinosis syndrome. Dermatol Online J 2007;13:22.

VII. Serrano A, Rodriguez L, Conejo-Mir J. Mucinosis eritematosa reticular. Actas Dermosifiliogr 2004;95:317-319.

VIII. Braddock SW, Davis CS, Davis RB. Reticular erythematous mucinosis and thrombocytopenic purpura. Report of a case and review of the world literature, including plaquelike cutaneous mucinosis. J Am Acad Dermatol 1988;19:859-868.

IX. Rongioletti F, Merlo V, Riva S, Cozzani E, et ál. Reticular erythematous mucinosis: a review of patients´s characteristics, associated conditions, therapy and outcome in 25 cases. Br J Dermatol 2013;169:1207-1211.

X. Cinotti E, Merlo V, Kempf W, Carli C, et ál. Reticular erythematous mucinosis: histopathological and immunohistochemical features of 25 patients compared with 25 cases of lupus erythematosus tumidus. J Eur Acad Dermatol Venereol 2015;29:689-697.

XI. Gruber R, Kuntz T, Oellig F, Paschos A, et ál. Retikuläre erythematöse Muzinose – Sonderform eines kutanen Lupus erythematodes? Z Rheumatol 2020;79:782-784.

Published

2020-12-30

Issue

Section

Original Articles