Porokeratosis of Mibelli in pediatric age

Authors

  • María Belén Cazorla Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Gisela Müller Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Mónica Yarza Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Daniel Navacchia Pathological Anatomy Division, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Susana Grees Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

DOI:

https://doi.org/10.47196/da.v26i1.2066

Keywords:

Porokeratosis, Porokeratosis of Mibelli

Abstract

Porokeratosis is a heterogeneous group of disorders in epidermal keratinization. It is an infrequent entity characterized clinically by hyperkeratotic papules that converge forming annular plaques with an atrophic center and raised borders. There are six clinical variants. The histopathological examination evidences the typical cornoid lamella. We present a 2-year-old girl diagnosed with porokeratosis of Mibelli and partial response to topical treatment of tretinoin 0,025%, still under clinical control.

Author Biographies

María Belén Cazorla, Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Resident Physician of Pediatric Dermatology. Pedro de Elizalde Hospital

Gisela Müller, Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Resident Physician of Pediatric Dermatology, Pedro de Elizalde Hospital

Mónica Yarza, Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Medical Doctor, Pediatric Dermatology Unit, Pedro de Elizalde Hospital

Daniel Navacchia, Pathological Anatomy Division, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Specialist in Pathology, Pathological Anatomy Division, Pedro de Elizalde Hospital

Susana Grees, Pediatric Dermatology Unit, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Head of the Pediatric Dermatology Unit, Pedro de Elizalde Hospital.

Director of the Career of Physicians Specialists in Pediatric Dermatology, Faculty of Medicine, University of Buenos Aires, Autonomous City of Buenos Aires, Argentina 

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Revista Dermatología Argentina Nº 1 de 2020

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Published

2020-03-02

Issue

Vol. 26 No. 1 (2020): January-March 2020

Section

Clinical Cases

License

El/los autor/es tranfieren todos los derechos de autor del manuscrito arriba mencionado a Dermatología Argentina en el caso de que el trabajo sea publicado. El/los autor/es declaran que el artículo es original, que no infringe ningún derecho de propiedad intelectual u otros derechos de terceros, que no se encuentra bajo consideración de otra revista y que no ha sido previamente publicado.

 

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