RACAND syndrome
Keywords:
RACAND syndrome, Raynaud phenomenon, anticentromere antibody, digital necrosis, systemic sclerosisAbstract
RACAND syndrome, an acronym for Raynaud’s phenomenon, anti-centromere antibody and digital necrosis, is a poorly known entity. We present a patient with RF-associated digital necrosis that progressed despite treatment with vasodilators. She also performed hyperbaric oxygen therapy and prostaglandin E1. She added sclerosis so she received methotrexate and bosentan. We show its complete evolution.
This syndrome must be taken into account as a differential diagnosis in acute digital necrosis, with a multidisciplinary diagnostic and therapeutic approach, which requires aggressive treatment from the beginning and subsequent follow-up due to possible transformation to systemic sclerosis.
References
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