Langerhans cell histiocytosis congenital with single lesion

Authors

  • María Emilia Villani General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina
  • María Rueda Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Daniela Espósito General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina
  • Daniel Navacchia Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Susana Grees Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Keywords:

Langerhans cell histiocytosis, congenital histiocytosis

Abstract

Langerhans cell histiocytosis have as a common characteristic the proliferation of dendritic antigen presenting cells with phenotypical and ultrastructural characteristics of Langerhans cells. Infiltration may be limited to one organ or may be disseminated.

Author Biographies

María Emilia Villani, General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina

Medical Dermatologist and Pediatric Dermatologist Staff

María Rueda, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Pediatric dermatologist

Daniela Espósito, General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina

Medical Dermatologist

Daniel Navacchia, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Pathologist, Head of the Department of Central Services, Diagnosis and Treatment

Susana Grees, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Head of the Dermatology Unit

References

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VIII. Gothwhal S, Gupta AK, Choudhary R. Congenital self-healing Langerhans cell histiocytosis. Indian J Pediatr 2018;316-317.

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Published

2019-06-20

Issue

Section

Clinical Cases