Epithelioid hemangioendothelioma

Authors

  • Olidiz De Luque Montaño Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina
  • María Irina González Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina
  • Mirta Morichelli Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina
  • Inés Stella Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina

DOI:

https://doi.org/10.47196/2ttmr934

Keywords:

cutaneous epithelioid hemangioendothelioma, vascular tumors, immunohistochemistry

Abstract

Cutaneous epithelioid hemangioendothelioma is a rare malignant vascular tumor. It was described in 1986 by Sharon Weiss and Franz Enziger and previously considered intermediate aggressive, but its high metastatic capacity justifies its inclusion in the group of malignant lesions. It usually appears in adolescents and young adults.  It usually affects soft tissues and less frequently the lung and liver. The diagnosis is histological and the epithelioid appearance of the neoplastic endothelial cells and the tendency to form vascular channels are characteristic. Treatment is surgery with wide margins. This tumor exceptionally affects the skin, with few cases, described in the medical literature.

Author Biographies

  • Olidiz De Luque Montaño, Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina

    Attending Physician, Dermatology Department

  • María Irina González, Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina

    Staff Physician, Department of Dermatology

  • Mirta Morichelli, Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina

    Head of Department, Department of Dermatology

  • Inés Stella, Bernardino Rivadavia General Acute Care Hospital, City of Buenos Aires, Argentina

    Specialist Physician in Anatomic Pathology, Department of Dermatology

References

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Published

2026-07-16

Issue

Vol. 32 No. 2 (2026): May–August

Section

Clinical Cases

License

Copyright (c) 2026 on behalf of the authors. Reproduction rights: Argentine Society of Dermatology

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