Kaposiform hemangioendothelioma
DOI:
https://doi.org/10.47196/da.v31i2.2878Keywords:
kaposiform hemangioendothelioma, vascular tumorsAbstract
Kaposiform hemangioendothelioma (KHE) is a locally aggressive, rare vascular tumor that affects pediatric patients. It presents as a firm and solitary tumor, erythematous-purple, located in the skin or soft tissue, that can invade adipose tissue muscle and bone. Approximately 70% of cases may be associated with the Kasabach-Merritt phenomenon, a consumptive coagulopathy that carries significant morbidity and mortality. Due to the lack of a standardized treatment, several therapeutic options have been explored, including corticosteroid therapy, sirolimus, and vincristine. We present the case of a preterm newborn patient with KHE diagnosis.
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