Epithelioid sarcoma: two variants of the same entity

Authors

  • Luca Garin Troyer General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Valeria Cecilia Orsi J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Ana Campastri J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Iris Barrio J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • César Chiappe J.M. Ramos Mejía Acute Hospital General, Autonomous City of Buenos Aires, Argentina
  • Guadalupe Ailín García General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Paula Bourren Dr. Juan A. Fernández General Acute Hospital, Autonomous City of Buenos Aires, Argentina
  • Cecilia Eleonora Ventrice General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina
  • Ana Clara Acosta J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

Keywords:

sarcomas, epithelioid sarcoma, INI1, SMARCB1

Abstract

Sarcomas are malignant neoplasms that originate from mesenchymal tissue. Epithelioid sarcoma is a rare variant of soft tissue sarcoma, representing approximately 1% of them. There are two variants: a distal type and a proximal one, with a high recurrence and metastasis rate.

Two cases of male patients with epithelioid sarcoma are presented, one with the distal variant and the other with the proximal variant.

Author Biographies

  • Luca Garin Troyer, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

    Dermatologist, Department of Dermatology and Pathology

  • Valeria Cecilia Orsi, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

    Second Year Resident Physician, Dermatology and Pathology Service

  • Ana Campastri, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

    Dermatologist, Department of Dermatology and Pathology

  • Iris Barrio, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

    Dermatologist. Staff Physician, Dermatology and Pathology Department

  • César Chiappe, J.M. Ramos Mejía Acute Hospital General, Autonomous City of Buenos Aires, Argentina

    Pathologist. Staff Physician, Dermatology and Pathology Service

  • Guadalupe Ailín García, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

    Medical Pathologist, Department of Dermatology and Pathology

  • Paula Bourren, Dr. Juan A. Fernández General Acute Hospital, Autonomous City of Buenos Aires, Argentina

    Dermatologist. Head of Service, Dermatology and Pathology Service

  • Cecilia Eleonora Ventrice, General Acute Hospital Dr. Juan A. Fernández, Autonomous City of Buenos Aires, Argentina

    Dermatologist and Pathologist. Staff Physician, Department of Dermatology and Pathology

  • Ana Clara Acosta, J.M. Ramos Mejía General Acute Hospital, Autonomous City of Buenos Aires, Argentina

    Dermatologist. Staff Physician, Dermatology and Pathology Department

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Published

2022-09-01

Issue

Vol. 28 No. 3 (2022): July-September 2022

Section

Original Articles

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