Eosinophilic angiocentric fibrosis, IgG-related head and neck disease

Authors

  • Hugo N. Cabrera Faculty of Medicine of the University of Buenos Aires, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
  • Silvia Pérez Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
  • María Fernanda Carriquiri Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina
  • José Casasꝉ Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

Keywords:

angiocentric fibrosis, IgG related disease

Abstract

Eosinophilic angiocentric fibrosis is a fibrosing inflammatory condition of the upper airways, sinuses, orbit, salivary and lacrimal glands, with cutaneous involvement usually over the nose; there is nasal deformation and obstruction, with erythematous plaques on its surface. It is of rare observation; less than 60 cases have been published, and it is included within the group of IgG4-related diseases. We present the case of an adult woman with facial skin involvement and respiratory obstructive symptoms, with normal serum IgG4, and a satisfactory response to methotrexate.

Author Biographies

  • Hugo N. Cabrera, Faculty of Medicine of the University of Buenos Aires, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

    Emeritus Professor of Dermatology

  • Silvia Pérez, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

    Dermatologist

  • María Fernanda Carriquiri, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

    Dermatologist

  • José Casasꝉ, Office of Prof. Dr. Hugo Cabrera, Autonomous City of Buenos Aires, Argentina

    Dermatopathologist

References

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Published

2022-09-01

Issue

Vol. 28 No. 3 (2022): July-September 2022

Section

Original Articles

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Copyright (c) 2022 on behalf of the authors. Reproduction rights: Argentine Society of Dermatology.

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