Langerhans cell histiocytosis congenital with single lesion

Authors

  • María Emilia Villani General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina
  • María Rueda Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Daniela Espósito General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina
  • Daniel Navacchia Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina
  • Susana Grees Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

Keywords:

Langerhans cell histiocytosis, congenital histiocytosis

Abstract

Langerhans cell histiocytosis have as a common characteristic the proliferation of dendritic antigen presenting cells with phenotypical and ultrastructural characteristics of Langerhans cells. Infiltration may be limited to one organ or may be disseminated.

Author Biographies

  • María Emilia Villani, General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina

    Medical Dermatologist and Pediatric Dermatologist Staff

  • María Rueda, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

    Pediatric dermatologist

  • Daniela Espósito, General Acute Hospital, Dr. Teodoro Álvarez, Autonomous City of Buenos Aires, Argentina

    Medical Dermatologist

  • Daniel Navacchia, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

    Pathologist, Head of the Department of Central Services, Diagnosis and Treatment

  • Susana Grees, Pedro de Elizalde Children's General Hospital, Autonomous City of Buenos Aires, Argentina

    Head of the Dermatology Unit

References

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V. Yurkovich M, Wong A, Lam JM. Solitary congenital self-healing Langerhans cell histiocytosis: a benign variant of Langerhans cells histiocytosis. Dermatol Online J 2013;19:3.

VI. Battistella M, Fraitag S, Teillac D, Brousse N, et ál. Neonatal and early infantile cutaneous Langerhans cell histiocytosis: comparision of self-regressive and non-seil-regressive forms. Arch Dermatol 2010;146:149-156.

VII. Mandel VD, Ferrari C, Cesinaro AM, Pellacani G, et ál. Congenital “self-healing” Langerhans cell histiocytosis (Hashimoto-Pritzker disease): a report of two cases with the same cutaneous manifestations but different clinical course. J Dermatol 2014;41:1098-1101.

VIII. Gothwhal S, Gupta AK, Choudhary R. Congenital self-healing Langerhans cell histiocytosis. Indian J Pediatr 2018;316-317.

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X. Yu J, Rubin AI, Castelo-Soccio L, Perman MJ. Congenital self-healing Langerhans cell histiocytosis. J Pediatr 2017; 84:232.

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Published

2019-06-20

Issue

Section

Clinical Cases