Vulvovaginal-gingival syndrome: a rare variant of erosive lichen planus
DOI:
https://doi.org/10.47196/xk7nrv50Keywords:
lichen planus, oral lichen planus, gingival diseases, vulvar diseases, vaginal diseases, vulvo-vaginal-gingival syndromeAbstract
The vulvo-vaginal-gingival syndrome (VVGS) is an uncommon variant of erosive lichen planus, characterized by the simultaneous involvement of the oral, vulvar, and vaginal mucosa. It may lead to severe scarring sequelae such as synechiae and dyspareunia, with a significant impact on the patient`s quality of life. Given its exclusively mucosal presentation and the frequent fragmentation of consultations among different specialties, it is likely underdiagnosed. We recommend an early, multidisciplinary diagnostic approach to prevent complications, improve prognosis, and reduce the physical and emotional burden on affected patients. We present a series of four adult women with painful oral and genital ulcers, and histopathological findings consistent with lichen planus. This study contributes to increasing the visibility of a rare variant of lichen planus and highlights the importance of systematic screening in clinical practice.
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