Angiosarcoma cutáneo: variantes clínicas

Resumen

El angiosarcoma es una neoplasia maligna poco frecuente que se origina en el endotelio vascular, de comportamiento agresivo local y a distancia. Su mortalidad es elevada. Se describen tres variantes cutáneas: idiopático (de la piel de la cara y cuero cabelludo o de Wilson Jones), secundario a linfedema crónico y posterior a tratamiento radiante.
Se presentan cuatro casos de angiosarcomas cutáneos evaluados en el servicio de dermatología del Policlínico Bancario. Se plantean diagnósticos diferenciales clínicos e histológicos.

(Dermatol. Argent., 2014, 20(1): 27-33).

Palabras clave: angiosarcoma cutáneo, síndrome de Stewart Treves,  linfedema, radioterapia.

Cutaneous angiosarcoma: clinical variants

Abstract
Angiosarcoma (AS) is a rare malignant neoplasm that originates from endothelial cells. It is locally and systemically aggressive and has a high rate of mortality. Three variants of cutaneous angiosarcoma are described: idiopathic (angiosarcoma of the scalp), secondary
to chronic limphedema and as a complication of radiation therapy.
We report four cases of cutaneous angiosarcoma, which were evaluated at the Dermatology Department at the Hospital “Policlínico Bancario”.
Clinical and histological differential diagnoses were described.

(Dermatol. Argent., 2014, 20(1): 27-33).

Keywords: angiosarcoma, Stewart Treves syndrome, lymphedema,
radiation treatment.